Cerebral hydatid disease (neurohydatidosis) is caused by Echinococcus granulosus or less commonly E. alveolaris or E. multilocularis. The larval stage is the cause of hydatid disease in humans 1. Epidemiology Cerebral hydatid disease is a rare parasitic infestation and accounts for 1-2 % of all cystic echinococcosis. Hydatid disease is endemic in the Mediterranean region, the Middle East, Africa, eastern part of Turkey, Australia and parts of South America 2. Clinical presentation Symptoms and signs include: focal neurological deficits headaches increased intracranial pressure hydrocephalus papilloedema and loss of vision altered mental status seizures (rare)